Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.
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Case report A 6-year-old female presented with a main complaint of a painless maxillary swelling which her parents noticed 8 months earlier. Compared with other 3 CODs, FGC takes on a really unique and aggressive form of behavior that is not supposed to be clinically approached in the giganitform framework of classification.
Please help improve this article by adding citations to reliable sources. In similar manner, large FGC lesion tends to plunder most calcium deposits and thereby extend itself with osseous growth. The ethical approval was granted by the Institutional Clinical Research Supervision Committee of our hospital. Cekentoma to the World Health Organization classification of osseous dysplasias ODFGC is generally regarded as an odontogenic lesion that shares a same periodontal ligament origin with focal, periapical.
Fibro-osseous lesions of the face and jaws. Journal List Dentomaxillofac Radiol v. Articles lacking sources from December All articles lacking sources Infobox medical condition All stub articles. Microscopic examination showed a lobular calcified mass with a peripheral zone of fibropsammomatous tissue corresponding with the radiolucent margin. The swelling depressed the lower eyelid with exposure of the sclera, and expanded the palate.
A clinical and radiologic spectrum of cases.
Familial gigantiform cementoma: classification and presentation of a large pedigree.
Open in a separate window. Before referral, he had experienced 4 times of fractures in bilateral lower extremities within 4 years. Besides, the informed consent was obtained from these patients. The objective of this report is to present an unusual case of a gigantiform cemenhoma manifesting with gross expansion of the maxilla in a 6-year-old black female. Cementoma Search for additional papers on this topic.
In addition, FGC also carries a striking tendency toward more exuberant growth with multiquadrant jaw involvement. Microscopic examination showed mineralized bone with obliterated marrow spaces containing inactive fibrous tissue Figure 5. Osteomas are more common in the craniofacial bones than in other parts of the skeleton. Cemento-osseous dysplasia of the jaw bones: Macdonald Oral surgery, oral medicine, oral pathology and….
However, the management of the expansive FGCs entails complete surgical removal at an early stage of growth in order to limit the extent of surgery and prevent tooth displacement and loss of residual bone.
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Gigantiform cementoma in a child
Gigantifogm differential diagnoses, which include osteoma, ossifying fibroma and cementoblastoma, are discussed. The radiological differential diagnosis of a well-defined, expansive mineralized mass in the jawbone includes benign cementoblastoma, osteoma, ossifying fibroma and FGC.
FGC is uncommon, occurs predominantly in young patients and has the potential to cause considerable jaw expansion. We are determined to keep this website freely accessible.
Pediatr Blood Cancer ; ArmstrongPeter Dirks Journal of neurosurgery. Distinguishing features of focal cemento-osseous dysplasia and cemento-ossifying fibromas. Support Center Support Center. Surgery with recontouring and shaving intent was initially attempted in a local institution about 7 months ago, but in vain. Radiographs of fracture areas in 1 patient showed osteopenic bone and excess callus formation.